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Indicatori PNS 2025 / Boli rare-nr bolnavi-TRIM I 2025.xlsx
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NUMAR BOLNAVI boli rare
L2 Programul naţional de tratament pentru boli rare
L3 Situaţia indicatorilor fizici realizaţi în perioada 01.01.2025-31.03.2025
L7 CAS Număr bolnavi cu boli rare cărora li s-au eliberat medicamente/materiale sanitare prin farmaciile cu circuit închis, pentru: Număr bolnavi cu boli rare cărora li s-au eliberat medicamente prin farmaciile cu circuit deschis, pentru:
L8 Boli neurologice degenerative/ inflamator-imune forme cronice Boli neurologice degenerative/ inflamator-imune forme acute Boala Fabry Boala Pompe Tirozinemie Mucopolizaharidoză tip II (sindromul Hunter) Mucopolizaharidoză tip I (sindromul Hurler) Afibrinogenemie congenitală Sindrom de imunodeficienţă primară HTPA Amiloidoză cu transtiretină: Scleroză sistemică şi ulcerele digitale evolutive Purpura trombocitopenică imună cronică Hiprerfenilalaninemie la bolnavii diagnosticaţi cu fenilcetonurie sau deficit de tetrahidrobiopterină (BH4) Scleroza tuberoasă Osteogeneză imperfectă Epidermoliză buloasă Atrofie musculară spinală Boala Castelman Mucopolizaharidoza Tip IVA Lipofuscinoza ceroida TIP 2 (TPP1) Sindrom hemolitic uremic atipic (SHUa) Hemoglobinurie paroxistică nocturnă(HPN) Deficit de sfingomielinază acidă (DSMA) Mucoviscidoză copii Mucoviscidoză adulţi Scleroză laterală amiotrofică Sindrom Prader Willi fibroză pulmonară idiopatică distrofie musculară Duchenne angioedem ereditar Neuropatie optică ereditară Leber Limfangioleiomiomatoză Purpura trombocitopenică imună cronică Boala Fabry Atrofie musculară spinală
L9 afectare neurologică afectare cardiacă sau formă mixtă medicamente materiale sanitare Total medicamente materiale sanitare Total bolnav adult / copil cu greutate > 40 Kg bolnav copil cu greutate < 40 Kg
L10 C0 C1 C2 C3 C4 C5 C6 C7 C8 C9 C10 C11 C12 C13 C14 C15 C16 C17 C18 C19 C20 C21 C22 C23 C24 C25 C26 C27 C28 C29 C30 C31 C32 C33 C34 C35 C36 C37 C38 C39 C40 C41 C42
L11 Alba 4 4 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 4 3 12 1 4 0 2 0 0 1 0 3
L12 Arad 0 0 0 0 0 2 0 0 0 0 0 0 6 3 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 0 1 0 5 0 5 1 0 0 1 0 0 0
L13 Arges 0 0 4 0 1 1 0 0 0 0 0 0 0 11 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 6 4 14 1 3 0 4 0 0 1 0 6
L14 Bacau 10 7 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 5 2 14 0 4 0 1 0 0 1 0 0
L15 Bihor 17 3 0 0 0 0 1 0 4 15 0 0 0 3 5 0 0 0 0 0 0 0 0 0 0 0 1 0 0 0 12 3 21 0 3 1 4 0 0 11 0 2
L16 Bistrita-Nasaud 0 0 0 0 0 0 0 0 0 0 0 0 0 10 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 2 0 5 0 5 0 0 0 0 1 0 0
L17 Botosani 0 0 0 0 0 0 0 0 0 0 0 0 0 3 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 7 2 3 0 3 0 0 0 0 0 0 2
L18 Brasov 0 0 3 0 0 1 0 0 14 0 0 0 0 3 0 4 0 0 0 0 0 0 0 1 0 0 0 0 0 0 37 9 19 0 4 0 2 0 0 5 0 5
L19 Braila 0 1 0 0 0 2 0 0 0 0 0 0 0 4 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 11 1 8 1 0 1 0 1 0 7 0 0
L20 Buzau 0 0 0 0 0 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 2 9 0 1 0 0 1 0 2 0 0
L21 Caras-Severin 0 0 0 1 0 0 0 0 0 0 0 0 0 5 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 2 7 0 0 1 0 0 0 0 0 0
L22 Calarasi 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 4 1 1 0 0 0 2 0 0 0 0 0
L23 Cluj 42 19 3 0 0 0 0 0 88 163 0 12 38 65 10 5 0 0 0 21 23 23 3 8 0 0 3 2 1 2 4 8 22 3 26 0 0 4 0 23 0 6
L24 Constanta 16 9 1 2 1 0 0 0 0 0 0 0 7 5 0 0 0 0 0 0 0 0 4 0 0 0 0 0 0 0 19 7 22 0 9 1 3 0 1 7 0 2
L25 Covasna 0 0 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 7 7 9 0 2 0 0 0 0 1 0 1
L26 Dambovita 0 0 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 8 6 9 0 0 0 5 2 0 2 0 4
L27 Dolj 0 0 3 1 0 1 0 0 2 0 0 0 13 0 0 0 0 0 0 0 0 0 0 0 0 0 1 0 2 1 8 3 10 1 3 2 0 0 2 16 1 3
L28 Galati 0 5 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 5 9 9 0 6 1 0 0 0 1 0 1
L29 Giurgiu 0 0 0 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 3 1 0 1 0 0 0 0 0 0 0 0
L30 Gorj 0 0 0 0 0 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 4 1 8 0 2 0 0 0 0 2 0 4
L31 Harghita 5 0 0 0 0 0 0 0 2 0 0 0 9 10 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 2 2 8 0 1 0 1 0 0 2 0 1
L32 Hunedoara 0 0 0 0 0 0 0 0 2 0 0 0 0 9 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 0 5 1 8 0 6 0 0 0 1 0 0 0
L33 Ialomita 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 2 2 1 0 2 0 0 1 0 1 0 4
L34 Iasi 15 11 4 1 0 0 0 0 16 54 0 20 23 30 1 6 0 1 1 17 29 29 1 0 0 0 6 15 5 6 18 15 10 0 7 0 0 4 1 12 3 0
L35 Maramures 14 3 0 0 0 0 0 0 18 0 0 2 0 82 0 0 0 0 0 0 0 0 0 0 0 0 1 0 0 2 5 1 10 0 13 0 1 1 0 13 0 2
L36 Mehedinti 1 4 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 0 7 0 2 0 0 0 0 4 0 3
L37 Mures 11 5 1 3 0 0 0 0 9 96 0 1 13 10 0 0 0 0 0 2 2 2 1 0 0 0 1 1 2 0 9 1 19 0 5 0 2 0 0 6 0 2
L38 Neamt 5 4 3 0 0 0 0 0 0 0 0 0 0 6 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 9 4 4 0 7 0 4 0 2 6 0 0
L39 Olt 0 0 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 3 4 0 2 0 9 0 1 0 0 2
L40 Prahova 0 0 0 0 0 0 0 0 0 0 0 0 0 9 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 21 11 17 1 3 0 2 0 0 14 0 0
L41 Satu Mare 3 1 1 0 0 0 0 0 2 0 0 4 0 4 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 2 6 12 0 5 0 2 0 0 1 0 0
L42 Salaj 0 0 0 0 0 0 0 0 0 0 0 0 0 2 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 4 0 5 0 2 0 0 0 0 1
L43 Sibiu 15 3 0 0 0 0 0 0 6 0 0 0 0 32 0 6 0 0 0 0 0 0 4 3 0 0 2 0 0 0 6 2 5 0 2 2 0 0 0 2 0 1
L44 Suceava 5 7 2 0 0 2 0 0 0 0 20 1 0 2 0 0 0 0 0 0 0 0 0 0 0 0 1 0 1 0 8 2 21 0 7 1 8 0 0 3 0 1
L45 Teleorman 0 0 0 0 0 2 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 5 4 4 0 0 0 0 0 0 1 0 2
L46 Timis 37 15 2 0 1 2 0 0 20 58 0 2 0 37 2 1 0 0 0 10 10 11 0 0 2 0 0 2 3 2 12 10 24 2 22 0 5 0 3 22 0 10
L47 Tulcea 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 8 1 0 0 0 1 1 0 0 0 0 0
L48 Vaslui 0 0 1 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 6 0 11 0 1 0 0 1 0 2 0 2
L49 Valcea 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 4 3 3 0 0 0 0 0 0 0 0 0
L50 Vrancea 0 0 5 0 0 0 0 0 0 0 0 0 0 10 0 0 0 0 0 0 0 0 0 0 0 0 0 0 1 0 6 0 12 0 2 0 3 0 1 1 1 1
L51 Bucuresti 121 56 16 1 0 1 0 0 31 288 4 25 99 98 10 60 0 0 0 15 18 18 24 9 1 4 27 5 23 6 31 46 65 5 54 1 13 1 2 50 0 11
L52 Ilfov 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 0 10 0 2 0 4 0 0 0 0 0 0 0
L53 AOPSNAJ 4 3 0 1 0 0 0 0 60 3 0 2 0 0 0 0 0 0 0 0 0 0 3 0 0 0 0 0 0 0 113 61 134 8 53 9 23 6 5 124 10 34
L54 Total =SUM(B11:B53) =SUM(C11:C53) =SUM(D11:D53) =SUM(E11:E53) =SUM(F11:F53) =SUM(G11:G53) =SUM(H11:H53) =SUM(I11:I53) =SUM(J11:J53) =SUM(K11:K53) =SUM(L11:L53) =SUM(M11:M53) =SUM(N11:N53) =SUM(O11:O53) =SUM(P11:P53) =SUM(Q11:Q53) =SUM(R11:R53) =SUM(S11:S53) =SUM(T11:T53) =SUM(U11:U53) =SUM(V11:V53) =SUM(W11:W53) =SUM(X11:X53) =SUM(Y11:Y53) =SUM(Z11:Z53) =SUM(AA11:AA53) =SUM(AB11:AB53) =SUM(AC11:AC53) =SUM(AD11:AD53) =SUM(AE11:AE53) =SUM(AF11:AF53) =SUM(AG11:AG53) =SUM(AH11:AH53) =SUM(AI11:AI53) =SUM(AJ11:AJ53) =SUM(AK11:AK53) =SUM(AL11:AL53) =SUM(AM11:AM53) =SUM(AN11:AN53) =SUM(AO11:AO53) =SUM(AP11:AP53) =SUM(AQ11:AQ53)
L55 Total/CNP 323 160 50 11 4 17 2 0 276 677 24 67 208 453 28 82 0 1 1 65 82 83 40 21 3 4 42 25 40 21 347 213 540 24 268 21 98 21 19 319 15 111
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